There are many neurodegenerative disorders caused by a dysfunction of organelles. A significant portion of genetic neurodegenerative disorders are believed to be caused by defects in lysosomes. The Batten diseases are relevant examples as they are due to defects in lysosomal enzymes. Common effects of these diseases include developmental delays, seizures, movement disorders, and intellectual disabilities. Which of the following describes an accurate scenario for a possible lysosomal storage disorder?